Distribution of Killer Cell Immunoglobulin–like Receptor (KIR) Genotypes in Patients with Familial Mediterranean Fever

Genotypic profiles of the natural killer cell immunoglobulin–like receptors (KIR) have been reported to vary among different ethnic groups and variable clinical entities. This study represents the first report on its distribution among patients with familial Mediterranean fever (FMF). We studied 56...

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Main Author: Khazen, Georges (author)
Other Authors: Khalaf, Roy A. (author), Mahfouz, Rami A.R. (author), Sabbagh, Amira S. (author), Shamseddine, Wael (author), Bazarbachi, Ali (author)
Format: article
Published: 2009
Online Access:http://hdl.handle.net/10725/3356
http://dx.doi.org/10.1089/gtmb.2008.0081
http://online.liebertpub.com/doi/pdf/10.1089/gtmb.2008.0081
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author Khazen, Georges
author2 Khalaf, Roy A.
Mahfouz, Rami A.R.
Sabbagh, Amira S.
Shamseddine, Wael
Bazarbachi, Ali
author2_role author
author
author
author
author
author_facet Khazen, Georges
Khalaf, Roy A.
Mahfouz, Rami A.R.
Sabbagh, Amira S.
Shamseddine, Wael
Bazarbachi, Ali
author_role author
dc.creator.none.fl_str_mv Khazen, Georges
Khalaf, Roy A.
Mahfouz, Rami A.R.
Sabbagh, Amira S.
Shamseddine, Wael
Bazarbachi, Ali
dc.date.none.fl_str_mv 2009
2016-03-17T13:17:00Z
2016-03-17T13:17:00Z
2016-03-17
dc.identifier.none.fl_str_mv 1945-0265
http://hdl.handle.net/10725/3356
http://dx.doi.org/10.1089/gtmb.2008.0081
Mahfouz, R. A., Sabbagh, A. S., Shamseddine, W., Bazarbachi, A., Ibrahim, G., Arayssi, T., ... & Khalaf, R. A. (2009). Distribution of Killer Cell Immunoglobulin–like Receptor (KIR) Genotypes in Patients with Familial Mediterranean Fever. Genetic testing and molecular biomarkers, 13(1), 91-95.
http://online.liebertpub.com/doi/pdf/10.1089/gtmb.2008.0081
dc.language.none.fl_str_mv en
dc.relation.none.fl_str_mv Genetic Testing and Molecular Biomarkers
dc.rights.*.fl_str_mv info:eu-repo/semantics/openAccess
dc.title.none.fl_str_mv Distribution of Killer Cell Immunoglobulin–like Receptor (KIR) Genotypes in Patients with Familial Mediterranean Fever
dc.type.none.fl_str_mv Article
info:eu-repo/semantics/publishedVersion
info:eu-repo/semantics/article
description Genotypic profiles of the natural killer cell immunoglobulin–like receptors (KIR) have been reported to vary among different ethnic groups and variable clinical entities. This study represents the first report on its distribution among patients with familial Mediterranean fever (FMF). We studied 56 unrelated Lebanese FMF patients, had their DNA typed using sequence-specific primer (SSP) technique for the presence of 16 KIR gene and pseudogene loci, and compared them to the general Lebanese population. The AA1 genotype was the most frequent in both the FMF and control groups. Six new KIR profiles were identified. The FMF group showed a higher prevalence of KIR 3DP1*003 (p < 0.05) and an increase in the BB genotype compared with controls. The results lead to an interesting future research question of whether or not KIR genotype is involved in the predisposition to or pathogenesis of FMF. This is the first report that describes the KIR genotypic profile in this important clinical disease.
eu_rights_str_mv openAccess
format article
id LAURepo_a919993e425faa158dbc129b6a75f3f8
identifier_str_mv 1945-0265
Mahfouz, R. A., Sabbagh, A. S., Shamseddine, W., Bazarbachi, A., Ibrahim, G., Arayssi, T., ... & Khalaf, R. A. (2009). Distribution of Killer Cell Immunoglobulin–like Receptor (KIR) Genotypes in Patients with Familial Mediterranean Fever. Genetic testing and molecular biomarkers, 13(1), 91-95.
language_invalid_str_mv en
network_acronym_str LAURepo
network_name_str Lebanese American University repository
oai_identifier_str oai:laur.lau.edu.lb:10725/3356
publishDate 2009
repository.mail.fl_str_mv
repository.name.fl_str_mv
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spelling Distribution of Killer Cell Immunoglobulin–like Receptor (KIR) Genotypes in Patients with Familial Mediterranean FeverKhazen, GeorgesKhalaf, Roy A.Mahfouz, Rami A.R.Sabbagh, Amira S.Shamseddine, WaelBazarbachi, AliGenotypic profiles of the natural killer cell immunoglobulin–like receptors (KIR) have been reported to vary among different ethnic groups and variable clinical entities. This study represents the first report on its distribution among patients with familial Mediterranean fever (FMF). We studied 56 unrelated Lebanese FMF patients, had their DNA typed using sequence-specific primer (SSP) technique for the presence of 16 KIR gene and pseudogene loci, and compared them to the general Lebanese population. The AA1 genotype was the most frequent in both the FMF and control groups. Six new KIR profiles were identified. The FMF group showed a higher prevalence of KIR 3DP1*003 (p < 0.05) and an increase in the BB genotype compared with controls. The results lead to an interesting future research question of whether or not KIR genotype is involved in the predisposition to or pathogenesis of FMF. This is the first report that describes the KIR genotypic profile in this important clinical disease.PublishedN/A2016-03-17T13:17:00Z2016-03-17T13:17:00Z20092016-03-17Articleinfo:eu-repo/semantics/publishedVersioninfo:eu-repo/semantics/article1945-0265http://hdl.handle.net/10725/3356http://dx.doi.org/10.1089/gtmb.2008.0081Mahfouz, R. A., Sabbagh, A. S., Shamseddine, W., Bazarbachi, A., Ibrahim, G., Arayssi, T., ... & Khalaf, R. A. (2009). Distribution of Killer Cell Immunoglobulin–like Receptor (KIR) Genotypes in Patients with Familial Mediterranean Fever. Genetic testing and molecular biomarkers, 13(1), 91-95.http://online.liebertpub.com/doi/pdf/10.1089/gtmb.2008.0081enGenetic Testing and Molecular Biomarkersinfo:eu-repo/semantics/openAccessoai:laur.lau.edu.lb:10725/33562017-02-20T09:28:22Z
spellingShingle Distribution of Killer Cell Immunoglobulin–like Receptor (KIR) Genotypes in Patients with Familial Mediterranean Fever
Khazen, Georges
status_str publishedVersion
title Distribution of Killer Cell Immunoglobulin–like Receptor (KIR) Genotypes in Patients with Familial Mediterranean Fever
title_full Distribution of Killer Cell Immunoglobulin–like Receptor (KIR) Genotypes in Patients with Familial Mediterranean Fever
title_fullStr Distribution of Killer Cell Immunoglobulin–like Receptor (KIR) Genotypes in Patients with Familial Mediterranean Fever
title_full_unstemmed Distribution of Killer Cell Immunoglobulin–like Receptor (KIR) Genotypes in Patients with Familial Mediterranean Fever
title_short Distribution of Killer Cell Immunoglobulin–like Receptor (KIR) Genotypes in Patients with Familial Mediterranean Fever
title_sort Distribution of Killer Cell Immunoglobulin–like Receptor (KIR) Genotypes in Patients with Familial Mediterranean Fever
url http://hdl.handle.net/10725/3356
http://dx.doi.org/10.1089/gtmb.2008.0081
http://online.liebertpub.com/doi/pdf/10.1089/gtmb.2008.0081