Intrapulmonary Recombinant Factor VII as an Effective Treatment for Diffuse Alveolar Hemorrhage

Background: The diffuse alveolar hemorrhage (DAH) syndrome is a life-threatening pulmonary complication related to systemic vasculitides, posthematopoietic stem cell transplantation, drugs, or toxins. Once DAH develops, the mortality rate is as high as 50% to 80%. Initial treatment consists of high-...

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Main Author: Diab, Khalil J. (author)
Other Authors: Baker, Mary S. (author), Carlos, W. Graham (author), Mathur, Praveen (author)
Format: article
Published: 2016
Online Access:http://hdl.handle.net/10725/10031
http://dx.doi.org/10.1097/LBR.0000000000000286
http://libraries.lau.edu.lb/research/laur/terms-of-use/articles.php
https://oce.ovid.com/article/01436970-201607000-00016/HTML
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author Diab, Khalil J.
author2 Baker, Mary S.
Carlos, W. Graham
Mathur, Praveen
author2_role author
author
author
author_facet Diab, Khalil J.
Baker, Mary S.
Carlos, W. Graham
Mathur, Praveen
author_role author
dc.creator.none.fl_str_mv Diab, Khalil J.
Baker, Mary S.
Carlos, W. Graham
Mathur, Praveen
dc.date.none.fl_str_mv 2016
2019-02-13T11:10:42Z
2019-02-13T11:10:42Z
2019-02-13
dc.identifier.none.fl_str_mv 1944-6586
http://hdl.handle.net/10725/10031
http://dx.doi.org/10.1097/LBR.0000000000000286
Baker, M. S., Diab, K. J., Carlos, W. G., & Mathur, P. (2016). Intrapulmonary recombinant factor VII as an effective treatment for diffuse alveolar hemorrhage: a case series. Journal of bronchology & interventional pulmonology, 23(3), 255-258.
http://libraries.lau.edu.lb/research/laur/terms-of-use/articles.php
https://oce.ovid.com/article/01436970-201607000-00016/HTML
dc.language.none.fl_str_mv en
dc.relation.none.fl_str_mv Journal of Bronchology & Interventional Pulmonology
dc.rights.*.fl_str_mv info:eu-repo/semantics/openAccess
dc.title.none.fl_str_mv Intrapulmonary Recombinant Factor VII as an Effective Treatment for Diffuse Alveolar Hemorrhage
A Case Series
dc.type.none.fl_str_mv Article
info:eu-repo/semantics/publishedVersion
info:eu-repo/semantics/article
description Background: The diffuse alveolar hemorrhage (DAH) syndrome is a life-threatening pulmonary complication related to systemic vasculitides, posthematopoietic stem cell transplantation, drugs, or toxins. Once DAH develops, the mortality rate is as high as 50% to 80%. Initial treatment consists of high-dose steroids and supportive measures, including mechanical ventilation. We present a case series of 6 patients treated with intrapulmonary recombinant factor VIIa (rFVIIa) to treat refractory DAH. Methods: Six patients with DAH were treated with intrapulmonary instillation of rFVIIa. Doses were divided equally between the right and the left lungs. Doses were 30, 50, or 60 mcg/kg and frequencies varied from a single administration to repeated doses on subsequent days on the basis of the clinical response. All patients received high-dose steroids, and 4 also received an aminocaproic acid infusion. Results: Intrapulmonary rVFIIa treated DAH effectively in 5 of 6 patients. Doses used were smaller and less frequent than those described previously. Conclusions: Intrapulmonary factor VII is an effective adjunctive treatment for DAH. We achieved treatment success with both smaller and less frequent doses than those described previously. This may be a good therapeutic option for DAH, particularly when standard therapies have failed or bleeding is immediately life threatening. It is possible that intrapulmonary rFVIIa could save costs, while improving the intensive care unit length of stay. Further prospective studies are needed to assess the optimal dose and frequency for adequate therapeutic efficacy.
eu_rights_str_mv openAccess
format article
id LAURepo_c5ba6d5f5a694fe4df9b5d15a5e438c6
identifier_str_mv 1944-6586
Baker, M. S., Diab, K. J., Carlos, W. G., & Mathur, P. (2016). Intrapulmonary recombinant factor VII as an effective treatment for diffuse alveolar hemorrhage: a case series. Journal of bronchology & interventional pulmonology, 23(3), 255-258.
language_invalid_str_mv en
network_acronym_str LAURepo
network_name_str Lebanese American University repository
oai_identifier_str oai:laur.lau.edu.lb:10725/10031
publishDate 2016
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spelling Intrapulmonary Recombinant Factor VII as an Effective Treatment for Diffuse Alveolar HemorrhageA Case SeriesDiab, Khalil J.Baker, Mary S.Carlos, W. GrahamMathur, PraveenBackground: The diffuse alveolar hemorrhage (DAH) syndrome is a life-threatening pulmonary complication related to systemic vasculitides, posthematopoietic stem cell transplantation, drugs, or toxins. Once DAH develops, the mortality rate is as high as 50% to 80%. Initial treatment consists of high-dose steroids and supportive measures, including mechanical ventilation. We present a case series of 6 patients treated with intrapulmonary recombinant factor VIIa (rFVIIa) to treat refractory DAH. Methods: Six patients with DAH were treated with intrapulmonary instillation of rFVIIa. Doses were divided equally between the right and the left lungs. Doses were 30, 50, or 60 mcg/kg and frequencies varied from a single administration to repeated doses on subsequent days on the basis of the clinical response. All patients received high-dose steroids, and 4 also received an aminocaproic acid infusion. Results: Intrapulmonary rVFIIa treated DAH effectively in 5 of 6 patients. Doses used were smaller and less frequent than those described previously. Conclusions: Intrapulmonary factor VII is an effective adjunctive treatment for DAH. We achieved treatment success with both smaller and less frequent doses than those described previously. This may be a good therapeutic option for DAH, particularly when standard therapies have failed or bleeding is immediately life threatening. It is possible that intrapulmonary rFVIIa could save costs, while improving the intensive care unit length of stay. Further prospective studies are needed to assess the optimal dose and frequency for adequate therapeutic efficacy.PublishedN/A2019-02-13T11:10:42Z2019-02-13T11:10:42Z20162019-02-13Articleinfo:eu-repo/semantics/publishedVersioninfo:eu-repo/semantics/article1944-6586http://hdl.handle.net/10725/10031http://dx.doi.org/10.1097/LBR.0000000000000286Baker, M. S., Diab, K. J., Carlos, W. G., & Mathur, P. (2016). Intrapulmonary recombinant factor VII as an effective treatment for diffuse alveolar hemorrhage: a case series. Journal of bronchology & interventional pulmonology, 23(3), 255-258.http://libraries.lau.edu.lb/research/laur/terms-of-use/articles.phphttps://oce.ovid.com/article/01436970-201607000-00016/HTMLenJournal of Bronchology & Interventional Pulmonologyinfo:eu-repo/semantics/openAccessoai:laur.lau.edu.lb:10725/100312021-03-19T10:45:31Z
spellingShingle Intrapulmonary Recombinant Factor VII as an Effective Treatment for Diffuse Alveolar Hemorrhage
Diab, Khalil J.
status_str publishedVersion
title Intrapulmonary Recombinant Factor VII as an Effective Treatment for Diffuse Alveolar Hemorrhage
title_full Intrapulmonary Recombinant Factor VII as an Effective Treatment for Diffuse Alveolar Hemorrhage
title_fullStr Intrapulmonary Recombinant Factor VII as an Effective Treatment for Diffuse Alveolar Hemorrhage
title_full_unstemmed Intrapulmonary Recombinant Factor VII as an Effective Treatment for Diffuse Alveolar Hemorrhage
title_short Intrapulmonary Recombinant Factor VII as an Effective Treatment for Diffuse Alveolar Hemorrhage
title_sort Intrapulmonary Recombinant Factor VII as an Effective Treatment for Diffuse Alveolar Hemorrhage
url http://hdl.handle.net/10725/10031
http://dx.doi.org/10.1097/LBR.0000000000000286
http://libraries.lau.edu.lb/research/laur/terms-of-use/articles.php
https://oce.ovid.com/article/01436970-201607000-00016/HTML