Phosphorylated exogenous alpha-synuclein fibrils exacerbate pathology and induce neuronal dysfunction in mice

<p dir="ltr">Approximately 90% of alpha-synuclein (α-Synuclein) deposited in Lewy bodies is phosphorylated at serine 129 suggesting that the accumulation of phosphorylated α-Synuclein is critical in the pathogenesis of Parkinson’s disease. However, in vivo experiments addressing the...

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محفوظ في:
التفاصيل البيبلوغرافية
المؤلف الرئيسي: Mantia Karampetsou (8737815) (author)
مؤلفون آخرون: Mustafa T. Ardah (4858657) (author), Maria Semitekolou (2938959) (author), Alexia Polissidis (3040905) (author), Martina Samiotaki (438647) (author), Maria Kalomoiri (16874580) (author), Nour Majbour (3528548) (author), Georgina Xanthou (8344188) (author), Omar M. A. El-Agnaf (8809331) (author), Kostas Vekrellis (214282) (author)
منشور في: 2017
الموضوعات:
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author Mantia Karampetsou (8737815)
author2 Mustafa T. Ardah (4858657)
Maria Semitekolou (2938959)
Alexia Polissidis (3040905)
Martina Samiotaki (438647)
Maria Kalomoiri (16874580)
Nour Majbour (3528548)
Georgina Xanthou (8344188)
Omar M. A. El-Agnaf (8809331)
Kostas Vekrellis (214282)
author2_role author
author
author
author
author
author
author
author
author
author_facet Mantia Karampetsou (8737815)
Mustafa T. Ardah (4858657)
Maria Semitekolou (2938959)
Alexia Polissidis (3040905)
Martina Samiotaki (438647)
Maria Kalomoiri (16874580)
Nour Majbour (3528548)
Georgina Xanthou (8344188)
Omar M. A. El-Agnaf (8809331)
Kostas Vekrellis (214282)
author_role author
dc.creator.none.fl_str_mv Mantia Karampetsou (8737815)
Mustafa T. Ardah (4858657)
Maria Semitekolou (2938959)
Alexia Polissidis (3040905)
Martina Samiotaki (438647)
Maria Kalomoiri (16874580)
Nour Majbour (3528548)
Georgina Xanthou (8344188)
Omar M. A. El-Agnaf (8809331)
Kostas Vekrellis (214282)
dc.date.none.fl_str_mv 2017-11-28T03:00:00Z
dc.identifier.none.fl_str_mv 10.1038/s41598-017-15813-8
dc.relation.none.fl_str_mv https://figshare.com/articles/journal_contribution/Phosphorylated_exogenous_alpha-synuclein_fibrils_exacerbate_pathology_and_induce_neuronal_dysfunction_in_mice/27088018
dc.rights.none.fl_str_mv CC BY 4.0
info:eu-repo/semantics/openAccess
dc.subject.none.fl_str_mv Biomedical and clinical sciences
Neurosciences
Alpha-synuclein (α-Synuclein)
Parkinson’s disease
Phosphorylation
Lewy bodies
Stereotaxic injections
Neurodegeneration
dc.title.none.fl_str_mv Phosphorylated exogenous alpha-synuclein fibrils exacerbate pathology and induce neuronal dysfunction in mice
dc.type.none.fl_str_mv Text
Journal contribution
info:eu-repo/semantics/publishedVersion
text
contribution to journal
description <p dir="ltr">Approximately 90% of alpha-synuclein (α-Synuclein) deposited in Lewy bodies is phosphorylated at serine 129 suggesting that the accumulation of phosphorylated α-Synuclein is critical in the pathogenesis of Parkinson’s disease. However, in vivo experiments addressing the role of phosphorylated α-Synuclein in the progression of Parkinson’s disease have produced equivocal data. To clarify a role of Ser129 phosphorylation of α-Synuclein in pathology progression we performed stereotaxic injections targeting the mouse striatum with three fibrilar α-Synuclein types: wt-fibrils, phosphorylated S129 fibrils and, phosphorylation incompetent, S129A fibrils. Brain inoculation of all three fibrilar types caused seeding of the endogenous α-Synuclein. However, phosphorylated fibrils triggered the formation of more α-Synuclein inclusions in the Substantia Nigra pars compacta (SNpc), exacerbated pathology in the cortex and caused dopaminergic neuronal loss and fine motor impairment as early as 60 days post injection. Phosphorylated fibril injections also induced early changes in the innate immune response including alterations in macrophage recruitment and IL-10 release. Our study further shows that S129 phosphorylation facilitated α-Synuclein fibril uptake by neurons. Our results highlight the role of phosphorylated fibrilar α-Synuclein in pathology progression in vivo and suggest that targeting phosphorylated α-Synuclein assemblies might be important for delaying inclusion formation.</p><h2>Other Information</h2><p dir="ltr">Published in: Scientific Reports<br>License: <a href="https://creativecommons.org/licenses/by/4.0" target="_blank">https://creativecommons.org/licenses/by/4.0</a><br>See article on publisher's website: <a href="https://dx.doi.org/10.1038/s41598-017-15813-8" target="_blank">https://dx.doi.org/10.1038/s41598-017-15813-8</a></p>
eu_rights_str_mv openAccess
id Manara2_93ba161f3939c51b32dd3b2db30d21d2
identifier_str_mv 10.1038/s41598-017-15813-8
network_acronym_str Manara2
network_name_str Manara2
oai_identifier_str oai:figshare.com:article/27088018
publishDate 2017
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spelling Phosphorylated exogenous alpha-synuclein fibrils exacerbate pathology and induce neuronal dysfunction in miceMantia Karampetsou (8737815)Mustafa T. Ardah (4858657)Maria Semitekolou (2938959)Alexia Polissidis (3040905)Martina Samiotaki (438647)Maria Kalomoiri (16874580)Nour Majbour (3528548)Georgina Xanthou (8344188)Omar M. A. El-Agnaf (8809331)Kostas Vekrellis (214282)Biomedical and clinical sciencesNeurosciencesAlpha-synuclein (α-Synuclein)Parkinson’s diseasePhosphorylationLewy bodiesStereotaxic injectionsNeurodegeneration<p dir="ltr">Approximately 90% of alpha-synuclein (α-Synuclein) deposited in Lewy bodies is phosphorylated at serine 129 suggesting that the accumulation of phosphorylated α-Synuclein is critical in the pathogenesis of Parkinson’s disease. However, in vivo experiments addressing the role of phosphorylated α-Synuclein in the progression of Parkinson’s disease have produced equivocal data. To clarify a role of Ser129 phosphorylation of α-Synuclein in pathology progression we performed stereotaxic injections targeting the mouse striatum with three fibrilar α-Synuclein types: wt-fibrils, phosphorylated S129 fibrils and, phosphorylation incompetent, S129A fibrils. Brain inoculation of all three fibrilar types caused seeding of the endogenous α-Synuclein. However, phosphorylated fibrils triggered the formation of more α-Synuclein inclusions in the Substantia Nigra pars compacta (SNpc), exacerbated pathology in the cortex and caused dopaminergic neuronal loss and fine motor impairment as early as 60 days post injection. Phosphorylated fibril injections also induced early changes in the innate immune response including alterations in macrophage recruitment and IL-10 release. Our study further shows that S129 phosphorylation facilitated α-Synuclein fibril uptake by neurons. Our results highlight the role of phosphorylated fibrilar α-Synuclein in pathology progression in vivo and suggest that targeting phosphorylated α-Synuclein assemblies might be important for delaying inclusion formation.</p><h2>Other Information</h2><p dir="ltr">Published in: Scientific Reports<br>License: <a href="https://creativecommons.org/licenses/by/4.0" target="_blank">https://creativecommons.org/licenses/by/4.0</a><br>See article on publisher's website: <a href="https://dx.doi.org/10.1038/s41598-017-15813-8" target="_blank">https://dx.doi.org/10.1038/s41598-017-15813-8</a></p>2017-11-28T03:00:00ZTextJournal contributioninfo:eu-repo/semantics/publishedVersiontextcontribution to journal10.1038/s41598-017-15813-8https://figshare.com/articles/journal_contribution/Phosphorylated_exogenous_alpha-synuclein_fibrils_exacerbate_pathology_and_induce_neuronal_dysfunction_in_mice/27088018CC BY 4.0info:eu-repo/semantics/openAccessoai:figshare.com:article/270880182017-11-28T03:00:00Z
spellingShingle Phosphorylated exogenous alpha-synuclein fibrils exacerbate pathology and induce neuronal dysfunction in mice
Mantia Karampetsou (8737815)
Biomedical and clinical sciences
Neurosciences
Alpha-synuclein (α-Synuclein)
Parkinson’s disease
Phosphorylation
Lewy bodies
Stereotaxic injections
Neurodegeneration
status_str publishedVersion
title Phosphorylated exogenous alpha-synuclein fibrils exacerbate pathology and induce neuronal dysfunction in mice
title_full Phosphorylated exogenous alpha-synuclein fibrils exacerbate pathology and induce neuronal dysfunction in mice
title_fullStr Phosphorylated exogenous alpha-synuclein fibrils exacerbate pathology and induce neuronal dysfunction in mice
title_full_unstemmed Phosphorylated exogenous alpha-synuclein fibrils exacerbate pathology and induce neuronal dysfunction in mice
title_short Phosphorylated exogenous alpha-synuclein fibrils exacerbate pathology and induce neuronal dysfunction in mice
title_sort Phosphorylated exogenous alpha-synuclein fibrils exacerbate pathology and induce neuronal dysfunction in mice
topic Biomedical and clinical sciences
Neurosciences
Alpha-synuclein (α-Synuclein)
Parkinson’s disease
Phosphorylation
Lewy bodies
Stereotaxic injections
Neurodegeneration