A Severe Case of Overlap of Morphea and Eosinophilic Fasciitis after Burn Injuries

<h3>Background</h3><p dir="ltr">Generalized morphea is a rare fibrosing skin illness that progresses from erythematous, violet‐colored skin patches to sclerotic plaques. Another uncommon immune‐mediated connective tissue disease called eosinophilic fasciitis (EF) evolves...

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محفوظ في:
التفاصيل البيبلوغرافية
المؤلف الرئيسي: Hania Sami (21436013) (author)
مؤلفون آخرون: Faria Sami (21436016) (author), Shahzad Ahmed Sami (21436019) (author), Abdulqadir J. Nashwan (11659453) (author)
منشور في: 2024
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author Hania Sami (21436013)
author2 Faria Sami (21436016)
Shahzad Ahmed Sami (21436019)
Abdulqadir J. Nashwan (11659453)
author2_role author
author
author
author_facet Hania Sami (21436013)
Faria Sami (21436016)
Shahzad Ahmed Sami (21436019)
Abdulqadir J. Nashwan (11659453)
author_role author
dc.creator.none.fl_str_mv Hania Sami (21436013)
Faria Sami (21436016)
Shahzad Ahmed Sami (21436019)
Abdulqadir J. Nashwan (11659453)
dc.date.none.fl_str_mv 2024-05-14T09:00:00Z
dc.identifier.none.fl_str_mv 10.1155/2024/3123953
dc.relation.none.fl_str_mv https://figshare.com/articles/journal_contribution/A_Severe_Case_of_Overlap_of_Morphea_and_Eosinophilic_Fasciitis_after_Burn_Injuries/29163266
dc.rights.none.fl_str_mv CC BY 4.0
info:eu-repo/semantics/openAccess
dc.subject.none.fl_str_mv Biomedical and clinical sciences
Clinical sciences
Immunology
Generalized morphea
Eosinophilic fasciitis (EF)
Autoimmune skin disease
Fibrosing disorders
Sclerotic skin plaques
Burn injury trigger
dc.title.none.fl_str_mv A Severe Case of Overlap of Morphea and Eosinophilic Fasciitis after Burn Injuries
dc.type.none.fl_str_mv Text
Journal contribution
info:eu-repo/semantics/publishedVersion
text
contribution to journal
description <h3>Background</h3><p dir="ltr">Generalized morphea is a rare fibrosing skin illness that progresses from erythematous, violet‐colored skin patches to sclerotic plaques. Another uncommon immune‐mediated connective tissue disease called eosinophilic fasciitis (EF) evolves to cause sclerosis and woody skin induration. The coexistence of the two is extremely rare and has a poorer prognosis. Our case report is one of the first to report burn injuries as a trigger factor for EF and generalized morphea overlap. </p><h3>Case Presentation</h3><p dir="ltr">A 36‐year‐old man presented with acute onset of rapidly progressing skin thickening, tender edema, and skin contractures involving all extremities, shortly after enduring burn injuries from a gasoline explosion. Workup was remarkable for peripheral eosinophilia, hypergammaglobulinemia, and elevated C‐reactive protein. Skin biopsy demonstrated sclerodermoid changes and sclerotic thickening of subcutaneous fibrous septa associated with stromal mucin, dermal perivascular, diffuse lymphoplasmacytic infiltrate with eosinophils, decreased CD34 expression, and increased factor XIIIa. He was subsequently diagnosed with an overlap of generalized morphea and eosinophilic fasciitis. The patient had only limited improvement with steroids, methotrexate, mycophenolate mofetil, and intralesional triamcinolone acetonide injections. </p><h3>Conclusion</h3><p dir="ltr">Generalized morphea with concomitant EF indicates some degree of therapeutic resistance and poor prognosis with a low quality of life. Burn injuries can be a trigger factor for this overlap syndrome. Prompt identification of at‐risk individuals and initiating aggressive management are necessary.</p><h2>Other Information</h2><p dir="ltr">Published in: Case Reports in Rheumatology<br>License: <a href="http://creativecommons.org/licenses/by/4.0/" target="_blank">http://creativecommons.org/licenses/by/4.0/</a><br>See article on publisher's website: <a href="https://dx.doi.org/10.1155/2024/3123953" target="_blank">https://dx.doi.org/10.1155/2024/3123953</a></p>
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identifier_str_mv 10.1155/2024/3123953
network_acronym_str Manara2
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oai_identifier_str oai:figshare.com:article/29163266
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spelling A Severe Case of Overlap of Morphea and Eosinophilic Fasciitis after Burn InjuriesHania Sami (21436013)Faria Sami (21436016)Shahzad Ahmed Sami (21436019)Abdulqadir J. Nashwan (11659453)Biomedical and clinical sciencesClinical sciencesImmunologyGeneralized morpheaEosinophilic fasciitis (EF)Autoimmune skin diseaseFibrosing disordersSclerotic skin plaquesBurn injury trigger<h3>Background</h3><p dir="ltr">Generalized morphea is a rare fibrosing skin illness that progresses from erythematous, violet‐colored skin patches to sclerotic plaques. Another uncommon immune‐mediated connective tissue disease called eosinophilic fasciitis (EF) evolves to cause sclerosis and woody skin induration. The coexistence of the two is extremely rare and has a poorer prognosis. Our case report is one of the first to report burn injuries as a trigger factor for EF and generalized morphea overlap. </p><h3>Case Presentation</h3><p dir="ltr">A 36‐year‐old man presented with acute onset of rapidly progressing skin thickening, tender edema, and skin contractures involving all extremities, shortly after enduring burn injuries from a gasoline explosion. Workup was remarkable for peripheral eosinophilia, hypergammaglobulinemia, and elevated C‐reactive protein. Skin biopsy demonstrated sclerodermoid changes and sclerotic thickening of subcutaneous fibrous septa associated with stromal mucin, dermal perivascular, diffuse lymphoplasmacytic infiltrate with eosinophils, decreased CD34 expression, and increased factor XIIIa. He was subsequently diagnosed with an overlap of generalized morphea and eosinophilic fasciitis. The patient had only limited improvement with steroids, methotrexate, mycophenolate mofetil, and intralesional triamcinolone acetonide injections. </p><h3>Conclusion</h3><p dir="ltr">Generalized morphea with concomitant EF indicates some degree of therapeutic resistance and poor prognosis with a low quality of life. Burn injuries can be a trigger factor for this overlap syndrome. Prompt identification of at‐risk individuals and initiating aggressive management are necessary.</p><h2>Other Information</h2><p dir="ltr">Published in: Case Reports in Rheumatology<br>License: <a href="http://creativecommons.org/licenses/by/4.0/" target="_blank">http://creativecommons.org/licenses/by/4.0/</a><br>See article on publisher's website: <a href="https://dx.doi.org/10.1155/2024/3123953" target="_blank">https://dx.doi.org/10.1155/2024/3123953</a></p>2024-05-14T09:00:00ZTextJournal contributioninfo:eu-repo/semantics/publishedVersiontextcontribution to journal10.1155/2024/3123953https://figshare.com/articles/journal_contribution/A_Severe_Case_of_Overlap_of_Morphea_and_Eosinophilic_Fasciitis_after_Burn_Injuries/29163266CC BY 4.0info:eu-repo/semantics/openAccessoai:figshare.com:article/291632662024-05-14T09:00:00Z
spellingShingle A Severe Case of Overlap of Morphea and Eosinophilic Fasciitis after Burn Injuries
Hania Sami (21436013)
Biomedical and clinical sciences
Clinical sciences
Immunology
Generalized morphea
Eosinophilic fasciitis (EF)
Autoimmune skin disease
Fibrosing disorders
Sclerotic skin plaques
Burn injury trigger
status_str publishedVersion
title A Severe Case of Overlap of Morphea and Eosinophilic Fasciitis after Burn Injuries
title_full A Severe Case of Overlap of Morphea and Eosinophilic Fasciitis after Burn Injuries
title_fullStr A Severe Case of Overlap of Morphea and Eosinophilic Fasciitis after Burn Injuries
title_full_unstemmed A Severe Case of Overlap of Morphea and Eosinophilic Fasciitis after Burn Injuries
title_short A Severe Case of Overlap of Morphea and Eosinophilic Fasciitis after Burn Injuries
title_sort A Severe Case of Overlap of Morphea and Eosinophilic Fasciitis after Burn Injuries
topic Biomedical and clinical sciences
Clinical sciences
Immunology
Generalized morphea
Eosinophilic fasciitis (EF)
Autoimmune skin disease
Fibrosing disorders
Sclerotic skin plaques
Burn injury trigger